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Scoliosis

Highlights

Overview

Scoliosis is an abnormal curving of the spine. Everyone's spine naturally curves a bit. But people with scoliosis have a spine that curves too much. The spine might look like the letter C or S.

Causes

Most of the time, the cause of scoliosis is unknown (idiopathic). Scoliosis can also be associated with congenital birth defects that cause a developing baby's spine to not form properly. Neuromuscular conditions are a third cause of scoliosis. These conditions include cerebral palsy, spinal bifida, and muscular dystrophy.

Risk Factors

Scoliosis affects both boys and girls, but girls are more at risk for curvature progression (worsening).
Scoliosis is usually first noticed when children experience growth spurts, typically around the ages of 10 to 15 years.

Diagnosis

The health care provider will ask the child to bend over to examine the alignment of the spine and tilt of hips and shoulder. Imaging tests such as x-rays, MRIs, or CT scans may be performed. The degree of curvature is measured using a technique called the Cobb angle.

Treatment

Treatment for scoliosis depends on various factors, including the child's age, skeletal growth, accompanying medical conditions, degree of curvature, and risk for progression (curve worsening).

Treatment options include:

Introduction

Scoliosis is an abnormal sideways curving of the spine. A normal spine has gentle natural curves that round the shoulders and make the lower back curve inward.

In scoliosis, the spine curves from side-to-side to varying degrees. Some of the spinal bones may rotate slightly, making the hips or shoulders appear uneven. In severe scoliosis, the twisting in the spine can pull the rib cage into the rotation.

Scoliosis typically causes the spine to curve in one of the following ways:

Scoliosis

Click the icon to see an image of scoliosis.

Scoliosis usually develops in the area between the upper back (the thoracic area) and lower back (lumbar area). It may also occur only in the upper or lower back.

The severity of scoliosis is determined by the extent of the spinal curve and the angle of the trunk rotation. It is usually measured in degrees. Curves of less than 20 degrees are considered mild and account for 80% of scoliosis cases. Curves that progress beyond 20 degrees need medical attention, usually involving periodic monitoring or bracing to make sure the condition is not becoming worse.

Other abnormalities of the spine that may occur alone or in combination with scoliosis include hyperkyphosis (an abnormal exaggeration in the backward rounding of the upper spine) and hyperlordosis (an exaggerated forward curving of the lower spine, also called swayback).

Kyphosis

Click the icon to see an image of kyphosis.

The Spine

Vertebrae. The spine is a column of small bones, or vertebrae, that support the entire upper body. The column is grouped into 3 sections of vertebrae:

Each vertebra is designated by a letter and a number. The letter reflects the region (C=cervical, T=thoracic, and L=lumbar), and the number signifies its location within that region. For example, C4 is the fourth vertebra down in the cervical region, and T8 is the eighth thoracic vertebra.

Below the lumbar region is the sacrum, a shield-shaped bony structure that connects with the pelvis at the sacroiliac joints. At the end of the sacrum are 2 to 4 tiny, partially fused vertebrae known as the coccyx or tailbone.

The Spinal Column and its Curves. The vertebrae combine to form the spinal column. When viewed from the side, in the upper trunk the column normally has a gentle outward curve (kyphosis) while the lower back has a reverse inward curve (lordosis).

The Disks. Vertebrae in the spinal column are separated from each other by small cushions of cartilage known as intervertebral disks. Inside each disk is a jelly-like substance, which is surrounded by a tough, fibrous ring. The disk is 80% water. This structure makes the disk both elastic and strong. The disks have no blood supply of their own, relying instead on nearby blood vessels to keep them nourished.

Processes. Each vertebra in the spine has a number of bony projections, known as processes. The processes attach to the muscles and ligaments in the back and act like little levers, allowing the spine to twist or bend.

Spinal Canal. Each vertebra and its processes surround and protect an arch-shaped central opening. These arches, aligned to run down the spine, form the spinal canal. The spinal canal encloses the spinal cord, the central trunk of nerves that connects the brain with the rest of the body.

skeletal spine

Click the icon to see an image of the bones of the spine.
Sacrum

Click the icon to see an image of the sacrum.
Spinal curves

Click the icon to see an image of spinal curves.
Intervertebral disk

Click the icon to see an image of an intervertabral disk.
Vertebrae

Click the icon to see an image of the vertebrae.

Causes

Scoliosis is often categorized into 2 types:

Idiopathic Scoliosis

In most cases, the cause of scoliosis is unknown (idiopathic). Because scoliosis often runs in families, researchers think that genetic factors may play a role. However, severity often varies widely among family members who have the condition, suggesting that other factors must be present.

Idiopathic scoliosis is classified based on age of presentation as:

Idiopathic scoliosis is sometimes initially diagnosed in adults during evaluation for other back complaints or disorders. The curve may or may not be significant.

Congenital Scoliosis

Congenital scoliosis is caused by birth defects that affect spine formation and result in deformed or fused vertebrae. Congenital scoliosis has a high likelihood of progressing in severity. Children usually require early surgical intervention to prevent serious complications.

In addition to spinal problems, children with congenital scoliosis also have a higher risk for organ deformities that can affect heart, kidney, urinary, and nervous system function.

Neuromuscular Scoliosis

Neuromuscular scoliosis results from a medical condition such as:

Neuromuscular conditions can cause paralysis or weaken the muscles that support the spine. The curves caused by neuromuscular scoliosis are usually severe, and affect the entire length of the spine. This type of scoliosis is often accompanied by a condition called pelvic obliquity in which the pelvis is tilted to one side.

People with neuromuscular scoliosis are at risk for significant complications, including lung and heart problems.

Causes of Scoliosis in Adults

Adult scoliosis has two primary causes:

Spina bifida (degrees of severity)

Spina bifida is a congenital disorder (present at birth) in which the backbone and spinal canal do not close before birth. In severe cases, this can result in the spinal cord and its covering membranes protruding out of an affected infant's back. Spina bifida may be nearly inconsequential, or it may be repairable through surgery.

Risk Factors

Age

Scoliosis is usually first diagnosed in children aged 10 to 15 years, around the time they are experiencing growth spurts.

Sex

Scoliosis affects both boys and girls. However, girls are more likely than boys to develop progression (worsening) of the curvature.

Family History

Scoliosis often run in families. If both parents have scoliosis, their children face a significantly higher risk than if only parent has the condition.

Medical Conditions

Certain type of genetic disorders, such as Marfan syndrome, can increase the risk for scoliosis. Medical conditions and injuries that affect the spine can increase risk.

Risk for Curve Progression

People who have curve angle greater than 25 degrees are at highest risk for scoliosis progression.

Prognosis

In general, the severity of the scoliosis depends on the degree of the curvature and whether it threatens vital organs, specifically the lungs and heart. Scoliosis is classified as:

In general, the older the child the less likely it is that the curve will progress. Scoliosis in a child under 10, for example, is more likely to progress than scoliosis in an adolescent. Girls tend to have a higher risk for progression than boys.

The location of the curve is also a factor. Thoracic curves, those in the upper spine, are more likely to progress than thoracolumbar curves or lumbar curves (those of the middle to lower spine).

The higher the degree of curvature the more likely the chance of progression and the more likely the lungs and respiratory function will be affected.

People with severe deformities, particularly those caused by underlying neuromuscular disorders, may develop restrictive thoracic disease. This term refers to breathing problems and trouble getting enough oxygen due to a deformity-related smaller chest cavity. The restricted chest cavity is also less able to expand when breathing.

Symptoms

Scoliosis is often painless and may not be noticed until a child reaches adolescence. It may appear in casual circumstances, such as a parent noticing that a hemline is uneven. Most cases of scoliosis develop very gradually.

When symptoms become apparent they may include:

Signs of scoliosis

Scoliosis may be suspected when one shoulder appears to be higher than the other, there is a curvature in the spine, or the pelvis appears to be tilted.

With more advanced scoliosis, fatigue may occur after prolonged sitting or standing. Scoliosis caused by muscle spasms or growths on the spine can sometimes cause pain. Severe scoliosis caused by neuromuscular conditions may have symptoms associated with trouble breathing.

Diagnosis

To diagnose scoliosis, the health care provider will take a detailed medical history and conduct a physical examination. Imaging tests may also be used to provide additional information.

Physical Examination

Adam's Forward Bend Test. The screening test used most often for diagnosing scoliosis is called the Adam's forward bend test.

The child bends forward, dangling the arms, with the feet together and knees straight. The curve of structural scoliosis is more apparent when bending over. In a child with scoliosis, the provider may observe an imbalanced rib cage, with one side higher than the other, or other deformities.

Forward bend test

The forward bend test is used most often in schools and medical offices to screen for scoliosis. During the test, the child bends forward with the feet together and knees straight while dangling the arms. Any imbalances in the rib cage or other deformities along the back could be a sign of scoliosis.

Other physical tests include:

Identifying the Curvature

A scoliometer, measures the angle of trunk inclination (ATI), which is also called the angle of trunk rotation (ATR). During this procedure:

Imaging Tests

Imaging tests are used to provide further information on curvature. They include x-rays, and more advanced imaging tests such as magnetic resonance imaging (MRI) and computed tomography (CT). MRIs and CT scans use 3-dimensional imaging. However, MRIs do not expose people to radiation.

MRI scans

Click the icon to see an image of an MRI.

Measuring the Extent of the Curve

The Cobb angle is the most commonly used method for determining and classifying the extent of the curve. It is calculated by:

Classifying Scoliosis

Scoliosis is diagnosed when the Cobb angles measures 11 degrees or more. The severity of scoliosis and need for treatment is usually determined by two factors:

Both factors are measured in degrees. These two factors are usually related. For example, a person with a spinal curve of 20 degrees will usually have an ATR of 5 degrees. However, most 20-degree curves do not get worse.

People do not usually need medical treatment until the curve reaches between 20 and 30 degrees, and the ATR is 7 degrees.

Treatment

The treatment choices for scoliosis are:

Decision to Treat or Wait

The general rule of thumb for treating scoliosis is to monitor and observe the condition if the curve is less than 20 degrees.

Curves greater than 25 degrees, or those that progress by 10 degrees while being monitored, may require brace treatment. Children who have severe scoliosis and are high risk for lung and heart problems may require immediate, aggressive treatment.

Choosing Braces or Surgery

In general, the following criteria are used to determine whether a child should receive a brace and conservative treatment or surgery:

The choice may not be so straightforward in certain cases, and it is important to discuss all options with your health care provider, including a doctor who specializes in orthopedics.

Braces

Braces are usually prescribed to prevent further progression of curves that are at least 25 degrees, and no more than 40 degrees. There should be documented progression of the curve, and the child should still be growing. A brace is generally used until the child's spine stops growing.

Braces are useful for idiopathic scoliosis. They are much less helpful for scoliosis caused by congenital or neuromuscular conditions. There is still uncertainty about which types of scoliosis curves are most likely to benefit from bracing.

Braces must be worn for at least 13 hours daily for positive results. Depending on your child's condition, the doctor may recommend wearing the brace for up to 23 hours a day. Some types of braces can be removed to accommodate participation in sports activities.

Scoliosis brace

A brace is one type of treatment for scoliosis. The brace works by exerting pressure on the back and ribs to push the spine into a straighter position. The brace usually fits snugly around the torso and can come in many styles. Improvements in design have been made in recent years. In a child who is still growing, bracing is usually recommended to help slow the progression of the curve. Ideally, the brace is worn almost full-time until the bones have stopped growing.

Team Approach

A team approach, involving several health professionals, helps support the child through the bracing process:

Types of Braces

There are 2 main types of braces:

Boston Brace. The thoracolumbar-sacral orthosis (TLSO), also called the Boston brace, is custom molded from plastic. It comes up to beneath the underarms and can be fitted close to the skin so that it does not show beneath clothing. TLSOs are used to treat mid-back and lower curves.

Milwaukee Brace. A full torso brace called the Milwaukee brace used to be the standard bracing treatment for scoliosis. It is still used, particularly for high curves in the upper part of the back. The brace is made from rigid plastic and has a neck ring with a chin rest and pad for the back of the head. Two metal vertical bars attach the neck ring to the body of the brace.

Other less common types of braces include:

It is not clear if these alternative types of braces are as effective as standard ones.

Braces and Compliance

In order for a brace to be effective, it needs to be worn regularly and for the prescribed hours. Children should have a brace that will be most effective for them, and have the lowest impact on their quality of life.

Young people often refuse to wear braces, even the newer models. Emotional support from family and professionals is extremely important to help a child accept the process and stay compliant with the treatment.

Physical Therapy

Physical therapy may be used along with bracing. A specific physical therapy approach called the Schroft method is designed specifically for people with scoliosis. It focuses improving posture, abdominal strength, flexibility, and breathing.

Surgery

Surgery for scoliosis is usually recommended for:

There are 4 main goals of scoliosis surgery:

It takes a 2-part process to accomplish these goals:

Different instruments, procedures, and surgical approaches are used to treat scoliosis. All of the operations require meticulous skill and should be performed by a surgeon specializing in spine surgery.

The cause of scoliosis often determines the type of procedure. Other determinants include:

You should always ask the surgeon and hospital about their experience with the specific procedures being considered.

Scoliosis surgery can take from 4 to 12 hours to perform. The child stays in the hospital for around 5 days, followed by 3 to 6 weeks of recovery time at home.

Before Surgery

Tell your child's surgeon what medicines your child is taking. This includes medicines, supplements, or herbs you bought without a prescription.

Before the operation your child will:

The surgeon or nurse will talk with you about having your child store some of his or her blood about a month before the surgery. This is so that your child's own blood can be used if a transfusion is needed during surgery.

During the 2 weeks before the surgery:

On the day of the surgery:

Surgical Approaches

The surgeon will make at least one surgical cut to get to your child's spine. This cut may be in your child's back, chest, or both places. The surgeon may also do the procedure using a special video camera.

The basic surgical approaches are:

Spinal Fusion Procedure

Most scoliosis operations involve fusing the vertebrae. The instruments and devices used to support the fusion vary.

Before surgery, your child will receive general anesthesia. This will make your child unconscious and unable to feel pain during the operation.

In the spinal fusion procedure, the surgeon will:

These grafts will regenerate, grow into the bone, and fuse the vertebrae together. Bone grafts will help keep the spine in the correct position.

Spinal fusion

Surgery for scoliosis involves correcting the curve (although not all the way) and fusing the bones in the curve together.

Bone grafts can be acquired from:

Instrumentation: During surgery, the surgeon will use steel rods attached to the spine by hooks, screws, or wires to straighten your child's spine and support the bones of the spine.

There are various types of instrumentation procedures. They include the Harrington procedure, the Coutrel-Doubousset procedure, and the Texas-Scottish-Rite Hospital instrumentation procedure.

The metal instruments are usually left in the body after the bone fuses together. In certain circumstances, a rod may need to be removed.

Complications

In addition to allergic reactions to anesthesia, infection, pain, and other standard surgical risks, specific complications associated with scoliosis surgery may include:

Problems that may develop in the future include:

Recovery and Outcomes

Your child's spine should look much straighter after surgery. There will still be some curve. It takes at least 3 months for the spinal bones to fuse together well. It will take 1 to 2 years for them to fuse completely. Children can resume many physical activities in the weeks and months after surgery, but will need to wait until the spine is fully healed before participating in contact sports.

Fusion stops growth in the spine. This is not usually a concern because most growth occurs in the long bones of the body, such as the leg bones. Children who have this surgery will probably gain height from both growth in the legs and from having a straighter spine.

Your child will be given pain medication in the hospital and will be discharged with a prescription for pain meds that can be taken for a few weeks. When prescription pain medication is stopped, the child can be given acetaminophen (Tylenol, generic) to cope with pain. Nonsteroidal anti-inflammatory drugs (NSAIDs), such as ibuprofen (Advil, generic), are not recommended because they may increase the risks for bleeding.

The health care team will give instructions to the parents about how to lift and move the child. For some types of procedures, the child may need to temporarily wear a brace to help prevent rotating movements that could delay recovery. During the initial weeks of recovery, the child should avoid movements that involve bending, lifting, or twisting.

Your child may need to see a physical therapist to receive an individualized exercise program that includes exercises for stretching and strengthening. An occupational therapist can provide exercises for activities of daily life, such as techniques for tying shoes, dressing, bathing, and cutting food.

Children can usually return to school about 1 month after spinal fusion surgery.

Other Types of Surgery

Growing Rod Technique. This technique is used for very young children in whom bracing has not helped. Instead of doing spinal fusion, a rod is surgically inserted into the child's back. The child will have surgery every 6 months to extend the rod so that the spine can continue to grow. Some growing rod techniques use a single rod, while others use 2 rods.

Vertebral Body Stapling and Anterior Spinal Tethering. Surgeons do these procedures using an anterior approach surgery without fusion. Vertebral body stapling is an experimental technique that may prevent curve progression in some young people with curves of less than 50 degrees. It involves stapling the outer curve on the side of the spine facing the chest, which helps stabilize and reduce progression of the inner curve. The procedure uses a special metal device that is clamp-shaped at body temperature. The device can be straightened when subjected to cold temperatures and inserted into the spine. When warmed up, the staple returns to its clamp shape and supports the spine.

Scoliosis Surgery in Adults. In most cases of adult scoliosis, nonsurgical care is preferred, if possible. This can include patient education, exercises, and medical treatments. Braces are not useful, and surgery is usually recommended as a last resort. In general, pain is the most common reason for scoliosis surgery in adults. A procedure such as disketomy (removal of a diseased disk) may be performed, followed by spinal fusion and instrumentation. However, adults have increased risks for complications of spinal fusion surgery.

Resources

References

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Review Date: 6/12/2015
Reviewed By: Dennis Ogiela, MD, Orthopedic Surgeon, Danbury Hospital, Danbury, CT. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Isla Ogilvie, PhD, and the A.D.A.M. Editorial team. Author: Julia Mongo, MS.
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